| | Disease Ontology | MeSH |
| Disease ID: | DOID:0050156 | D054990 |
| Disease Name: | idiopathic pulmonary fibrosis | Idiopathic Pulmonary Fibrosis |
| Category: | Disease Ontology | MeSH |
| Type: | | Respiratory Tract Diseases |
| Define: | A pulmonary fibrosis that is characterized by scarring of the lung. | A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change. |
| Alias: | FIBROCYSTIC PULMONARY DYSPLASIA//IDIOPATHIC PULMONARY FIBROSIS, FAMILIAL//cryptogenic fibrosing alveolitis | Idiopathic Pulmonary Fibrosis//Idiopathic Pulmonary Fibroses//Pulmonary Fibroses, Idiopathic//Idiopathic Fibrosing Alveolitis, Chronic Form//Fibrosing Alveolitis, Cryptogenic//Fibrocystic Pulmonary Dysplasia//Dysplasia, Fibrocystic Pulmonary//Fibrocystic Pulmonary Dysplasias//Pulmonary Dysplasia, Fibrocystic//Cryptogenic Fibrosing Alveolitis//Cryptogenic Fibrosing Alveolitides//Fibrosing Alveolitides, Cryptogenic//Pulmonary Fibrosis, Idiopathic//Familial Idiopathic Pulmonary Fibrosis//Idiopathic Pulmonary Fibrosis, Familial//Usual Interstitial Pneumonia//Interstitial Pneumonia, Usual//Usual Interstitial Pneumonias//Interstitial Pneumonitis, Usual//Pneumonitides, Usual Interstitial//Pneumonitis, Usual Interstitial//Usual Interstitial Pneumonitides//Usual Interstitial Pneumonitis |
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